Cutaneous features and diagnosis of primary Sjögren syndrome: An update and review - 19/09/18
Abstract |
Sjögren syndrome (SS) is an autoimmune connective tissue disorder (CTD) that principally affects the lacrimal and salivary glands. Although SS is 1 of the 3 most common autoimmune CTDs alongside systemic lupus erythematosus and progressive systemic sclerosis, it is the least researched CTD overall. SS poses a particular diagnostic challenge because it shares multiple clinical and immunologic features with other CTDs. However, there are some characteristic cutaneous clinical features that can precede the well-known sicca symptoms by years. By familiarizing themselves with these clinical features and having a high suspicion for SS, dermatologists can play an important role in the early diagnosis and treatment of this disease.
Le texte complet de cet article est disponible en PDF.Key words : annular erythema, anti-Ro (SS-A), cutaneous vasculitis, localized cutaneous nodular amyloidosis, sicca, Sjögren syndrome
Abbreviations used : ACR, AE, ANA, CTD, DIF, EULAR, LCNA, pSS, RA, SCLE, SS
Plan
Funding sources: None. |
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Conflicts of interest: None disclosed. |
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Reprints not available from the authors. |
Vol 79 - N° 4
P. 736-745 - octobre 2018 Retour au numéroBienvenue sur EM-consulte, la référence des professionnels de santé.
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