Association of anorectal malformation and intestinal malrotation - 05/05/15
Abstract |
Background |
Patients born with anorectal malformations (ARM) frequently have other congenital anomalies that are well-defined; however, limited data exist examining the relationship of ARM with malrotation.
Methods |
A 10-year retrospective review was performed to examine all patients treated at a regional children's medical center with a diagnosis of ARM. Data were collected to identify malrotation, vertebral, anorectal, cardiac, tracheo-esophageal fistula, renal, radial, limb (VACTERL) anomalies, the type of ARM, operative procedures performed, and long-term bowel management.
Results |
One hundred forty-six patients were identified. Upper gastrointestinal evaluation was performed in 21 patients (14.4%), while contrast enemas were performed in 22 patients (15.1%). Seven patients were found to have malrotation (4.8%) and 6/7 of these patients had 2 or more VACTERL anomalies.
Conclusions |
Patients with ARM and 2 or more VACTERL anomalies should undergo screening for malrotation. Patients with intestinal malrotation, ARM, and poor potential for bowel control should have their appendix preserved during a Ladd's procedure.
Le texte complet de cet article est disponible en PDF.Keywords : Anorectal malformation, Intestinal malrotation, Appendicostomy, Antegrade continence enema
Plan
Support for this study was provided by the National Center for Advancing Translational Sciences of the National Institutes of Health (UL1TR000423 and UL1TR000002). The content is solely the responsibility of the authors and does not necessarily represent the official views of the National Institutes of Health. |
Vol 209 - N° 5
P. 907-912 - mai 2015 Retour au numéroBienvenue sur EM-consulte, la référence des professionnels de santé.
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