Creation of a Neovagina in a Patient with Mayer-Rokitansky-Küster-Hauser (MRKH) Syndrome and Previously Corrected Rectovestibular Fistula Concomitant with Imperforate Anus - 05/04/15
, Zbigniew Friebe, MD, PhD, Kinga Iwaniec, MD, Witold Kędzia, MD, PhDAbstract |
Background |
Congenital absence of uterus and vagina (CAUV) when associated with anorectal malformations is usually diagnosed and repaired in infancy at the time of anorectoplasty. Long-term observations of patients are scarce and do not justify early vaginal reconstruction. Question arises whether creation of a neovagina can be safely and successfully performed when the patient is mature.
Case |
The patient, diagnosed with MRKH syndrome at 16 years of age, underwent repair of rectovestibular fistula and imperforate anus (“cut-back” procedure, temporal sigmostomy and sagittal anterior anorectoplasty) in infancy. At 18, modified Wharton vaginoplasty was performed with a good anatomico-functional outcome.
Summary and Conclusions |
Early repair of anorectal malformation and postponed vaginal reconstruction seem to be a viable option for patients with congenital rectovestibular fistula and anal atresia concomitant with CAUV.
Le texte complet de cet article est disponible en PDF.Key Words : Mayer-rokitansky-kuster-hauser syndrome, Anorectal malformation, Vaginal aplasia, Anal atresia
Plan
| The authors indicate no conflicts of interest. |
Vol 28 - N° 2
P. e17-e19 - avril 2015 Retour au numéro
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