Soft-tissue necrosis complicating tibial osteotomy in a child with Proteus syndrome - 22/03/14
, S. Bouchoucha, B. Hamdi, R. Boussetta, W. Saied, C. Jalel, M. Smida
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Abstract |
Introduction |
Proteus syndrome is a rare congenital hamartomatous disease frequently responsible for musculoskeletal deformities. The results and complications of surgical treatment are not well documented owing to the scarcity of reported cases.
Case report |
The authors report a case of poor evolution of valgus proximal tibial osteotomy in a 6-year-old girl with Proteus syndrome. The surgery was complicated by extensive deep wound necrosis exposing the tibial bone, necessitating surgical excision, antibiotherapy and controlled wound healing. At 1 year postoperatively, the deformity recurred.
Discussion |
The possibility of serious wound complications and of recurrence must be kept in mind when operating on a limb deformity in patients with Proteus syndrome. Potential complications should be taken into account in selecting the surgical correction technique: epiphysiodesis may be preferable to osteotomy.
Le texte complet de cet article est disponible en PDF.Keywords : Hemi-hypertrophy, Macrodactyly, Genu varum, Proteus syndrome
Plan
Vol 100 - N° 2
P. 251-254 - avril 2014 Retour au numéro
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