Endoscopic endonasal management of congenital intranasal meningocele in a 2-month-old infant - 06/12/13
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Summary |
Introduction |
Nasal meningocele, which is usually congenital, is a rare anomaly resulting from meningeal herniation into the nasal cavities through a bone defect in the skull base.
Case report |
An 8-day-old boy was referred with respiratory disturbance and nasal obstruction. Examination showed a cyst-like grayish swelling filling the right nasal cavity. CT scan showed opacity, of fluid-like density, filling the right nasal fossa, in contact with a small bony defect in the right cribriform plate. MRI ruled out herniated brain parenchyma and enabled diagnosis of meningocele. The patient was operated on at the age of 2months through a transnasal endoscopic approach. Immediate postoperative course was favorable. MRI control at 8months was normal.
Discussion |
Modern imaging (CT scan and MRI) is of paramount importance in the preoperative evaluation of nasal meningocele. Endoscopic endonasal (EE) surgery is currently the treatment of choice.
Conclusion |
Steady progress in instrumentation, technique and skills will increase the feasibility of skull-base surgery using an endonasal approach in the pediatric population.
Le texte complet de cet article est disponible en PDF.Keywords : Meningocele, Congenital, Skull base, Imaging, Endoscopic endonasal surgery
Plan
Vol 130 - N° 6
P. 345-347 - décembre 2013 Retour au numéroBienvenue sur EM-consulte, la référence des professionnels de santé.
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