Primary cutaneous Epstein-Barr virus–related lymphoproliferative disorders in 4 immunosuppressed children - 24/04/13
, Christine Bodemer, MD b, Stéphane Blanche, MD c, Eric Delabesse, MD d, Catherine Eschard, MD e, Nicole Brousse, MD a, Sylvie Fraitag, MD a
Reprint requests: Nadège Wallet-Faber, MD, Department of Pathology, Groupe Hospitalier Necker-Enfants Malades, 149 rue de Sèvres, 75743 Paris cedex 15, France.Abstract |
Primary cutaneous Epstein-Barr virus–related lymphoproliferative disorders are rare. We describe 4 cases in children: two with acquired immunodeficiencies (HIV infection, heart transplantation) and two with congenital immunodeficiencies (ataxia-telangiectasia and an undetermined disease affecting the T lymphocytes). Two of the lymphoproliferative disorders were T-cell types and two were B-cell types. The two T-cell types were also Epstein-Barr virus positive, which is extremely rare. Three of the patients developed extracutaneous disease with poor outcome, resulting in death.
Le texte complet de cet article est disponible en PDF.Abbreviations used : EBER, EBV, ISH, LMP, LPD, PCR, PTLD, TCR
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| Funding sources: None. |
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| Conflicts of interest : None declared. |
Vol 58 - N° 1
P. 74-80 - janvier 2008 Retour au numéro
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