Cystoid Macular Edema in Gyrate Atrophy of the Choroid and Retina: A Fluorescein Angiography and Optical Coherence Tomography Evaluation - 18/08/11
Résumé |
Purpose |
To analyze the importance f optical coherence tomography (OCT) to diagnose the cystoid macular edema in a case of gyrate atrophy.
Design |
Observational case report.
Methods |
A 12-year-old boy presenting with gyrate atrophy of the choroid and retina underwent ophthalmologic, clinical, and laboratory tests.
Results |
Plasma ornithine level was 735 μmol/l. Fluorescein angiography showed bilateral hyperfluorescence involving the central region of the macula. Optical coherence tomography (OCT) disclosed bilateral intraretinal cysts areas of low reflectivity with occasional high-signal elements bridging the retinal layers and intraretinal thickening.
Conclusions |
Both fluorescein angiography and OCT were helpful to confirm the diagnosis of macular involvement as a complication of gyrate atrophy of the choroid and retina in a patient who presented without any clinical evidence of cystoid macular edema, except a decrease in visual acuity.
Le texte complet de cet article est disponible en PDF.Vol 140 - N° 1
P. 147-149 - juillet 2005 Retour au numéroBienvenue sur EM-consulte, la référence des professionnels de santé.
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