Primary Neuroectodermal Tumor of Penis (PNET)—A Case Report - 09/08/11
Résumé |
Primary neuroectodermal tumor (PNET) is a rare entity with high malignant potential. It usually affects the skeletal system and primary extraskeletal involvement is uncommon. Because of rarity of tumor in the penis, only a few cases have been reported. A 17-year-old male adolescent presented with painless penile swelling of 4 weeks’ duration. Clinical examination revealed multiple, 1 cm hard nodules palpable on penile shaft. Open incisional biopsy of the penile nodule revealed an undifferentiated malignant round cell tumor and on immunohistochemistry a diagnosis of PNET was made. Metastatic workup was negative. Total penectomy and perineal urethrostomy was performed, and subsequently adjuvant chemotherapy was given.
Le texte complet de cet article est disponible en PDF.Plan
Vol 70 - N° 4
P. 811.e9-811.e10 - octobre 2007 Retour au numéroBienvenue sur EM-consulte, la référence des professionnels de santé.
L’accès au texte intégral de cet article nécessite un abonnement.
Déjà abonné à cette revue ?