Cystic Fibrosis Foundation Evidence-Based Guidelines for Management of Infants with Cystic Fibrosis - 07/08/11

Doi : 10.1016/j.jpeds.2009.09.001

Drucy Borowitz, MD ^a, Karen A. Robinson, PhD ^b, Margaret Rosenfeld, MD, MPH ^c, Stephanie D. Davis, MD ^d, Kathryn A. Sabadosa, MPH ^e, Stephanie L. Spear, PhD ^f, Suzanne H. Michel, MPH, RD, LDN ^g, Richard B. Parad, MD, MPH ^h, Terry B. White, PhD ⁱ, Philip M. Farrell, MD, PhD ^j, Bruce C. Marshall, MD ^i,^⁎ , Frank J. Accurso, MD ^k
^a Women and Children’s Hospital of Buffalo, State University of New York at Buffalo, NY
^b Johns Hopkins School of Medicine, Baltimore, MD
^c University of Washington, Seattle WA
^d University of North Carolina, Chapel Hill, NC
^e Dartmouth University, Hanover, NH
^f Cincinnati Children’s Hospital Medical Center, Cincinnati, OH
^g Children’s Hospital of Philadelphia, Philadelphia, PA
^h Brigham and Women’s Hospital, Boston, MA
ⁱ Cystic Fibrosis Foundation, Bethesda, MD
^j University of Wisconsin School of Medicine and Public Health, Madison, WI
^k Children’s Hospital, Denver, CO

Corresponding author: Dr Bruce Marshall, Cystic Fibrosis Foundation, 6931 Arlington Road, Bethesda, MD 20814.

Abstract

Newborn screening for cystic fibrosis (CF) offers the opportunity for early medical and nutritional intervention that can lead to improved outcomes. Management of the asymptomatic infant diagnosed with CF through newborn screening, prenatal diagnosis, or sibling screening is different from treatment of the symptomatically diagnosed individual. The focus of management is on maintaining health by preventing nutritional and respiratory complications. The CF Foundation convened a committee to develop recommendations based on a systematic review of the evidence and expert opinion. These guidelines encompass monitoring and treatment recommendations for infants diagnosed with CF and are intended to help guide families, primary care providers, and specialty care centers in the care of infants with CF.

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Mots-clés : AAP, BMI, CF, CFA, CFTR, CT, DHA, DRI, FE, FTT, MCT, NBS, OP, P&PD, PCP, PERT, PFT, PI, PS, RTC, RVRTC, RSV, USPSTF

Plan

Methods

Guidelines for the Care of Newly Diagnosed Infants with CF

Initial Visit

Coordination of Care with Primary Care Providers

Beyond the Initial Diagnosis

Micronutrients

Surveillance for Pulmonary Disease

Other Chronic Pulmonary Interventions

Future Research

Conclusion

Author Disclosures

Please see the Author Disclosures at the end of this article.

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Vol 155 - N° 6S

P. S73-S93 - décembre 2009 Retour au numéro

Article précédent

Improving the Care of Infants Identified through Cystic Fibrosis Newborn Screening
Bruce C. Marshall, Preston W. Campbell

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Management of Infants with Cystic Fibrosis: A Summary of the Evidence for the Cystic Fibrosis Foundation Working Group on Care of Infants with Cystic Fibrosis
Karen A. Robinson, Ian J. Saldanha, Naomi A. McKoy

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Cystic Fibrosis Foundation Evidence-Based Guidelines for Management of Infants with Cystic Fibrosis - 07/08/11

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