Fetal rhabdomyoma of the infratemporal fossa in children - 27/05/10

Doi : 10.1016/j.anorl.2010.02.008

N. Leboulanger ^a,^⁎ , A. Picard ^b, G. Roger ^a, E.N. Garabedian ^a
^a Inserm U-587, ENT and Head and Neck Surgery Dept, Armand-Trousseau Hospital, 26, rue du Dr-Arnold-Netter, 75012 Paris, France
^b The Plastic and Maxillofacial Surgery Department, Armand-Trousseau Hospital, 26, rue du Dr-Arnold-Netter, 75012 Paris, France

Corresponding author. Tel.: +0144736114; fax: +0144736108.

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Summary

Introduction

Fetal rhabdomyomas are very rare benign tumors with infrequent head and neck involvement. We present the first report of a case of a 3-year-old child with an infratemporal fossa location.

Material and methods

Case study.

Discussion

Given the volume of the tumor and its difficult-to-access location, medical treatment associating methotrexate and Velbé^® was proposed, but was not effective on the tumor volume after four courses. Surgical intervention via a combined intraoral and preauricular temporal approach allowed monoblock excision. There were no postoperative complications.

Conclusion

Medical treatment was unsuccessful. Surgical excision controlled the lesion with no recurrence since surgery. The main differential diagnosis is rhabdomyosarcoma.

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Keywords : Fetal rhabdomyoma, Infratemporal fossa, Child