Giant Juvenile Xanthogranuloma of face in an adult: A rare complexity - 29/09/22
Abstract |
Juvenile xanthogranuloma, a form of non-Langerhans cell histiocytosis can be defined as the proliferation of cells with macrophage like characteristics. It has been described as a benign, asymptomatic and common self-healing disorder of non-Langerhans cell histiocytosis (LCH), affecting mostly infants, children and rarely adults. We have documented a case of a 40 year old male who presented to us with extensive insidious papulonodulous growth over the face. The facial disfigurement caused was catastrophic. An extensive surgical excision and reconstruction was performed followed by histopathological evaluation. Microscopic study and immune histochemistry revaled Juvenile Xanthogranuloma of adult. The article highlights the presentation, diagnosis and management of this mammoth, rare disease.
Le texte complet de cet article est disponible en PDF.Keywords : Juvenile Xanthogranuloma, Adult onset, Facial disfigurement, Immunohistochemistry, Head and neck pathology
Plan
Financial Disclosure Statement: Dr. Richardson has nothing to disclose. No funding was received for this article. |
Vol 123 - N° 5
P. e364-e366 - octobre 2022 Retour au numéroBienvenue sur EM-consulte, la référence des professionnels de santé.
L’accès au texte intégral de cet article nécessite un abonnement.
Déjà abonné à cette revue ?